End-stage idiopathic pulmonary fibrosis (IPF) is a progressive and irreversible lung disease characterized by scarring of lung tissue, which leads to a decline in lung function over time. In end-stage IPF, the lung tissue becomes severely damaged, making it difficult for the lungs to supply oxygen to the body.
The symptoms of end-stage IPF can vary from person to person but may include:
- Severe shortness of breath, even at rest
- Chronic cough
- Rapid breathing
- Chest pain
- Fatigue and weakness
- Loss of appetite and weight loss
As the disease progresses, the lungs become less efficient at exchanging oxygen and carbon dioxide, leading to decreased oxygen levels in the blood. This can cause the following complications:
- Pulmonary hypertension (high blood pressure in the lungs)
- Respiratory failure
- Heart failure
- Pulmonary embolism (a blood clot in the lung)
- Pneumonia (lung infection)
- Respiratory distress syndrome (a life-threatening lung condition)
End-stage IPF is a serious condition that can significantly affect a person’s quality of life. Treatment options are limited, and the focus is on managing symptoms and improving quality of life. Palliative care can help manage symptoms and improve quality of life for people with end-stage IPF.
